Osteogenesis Imperfecta inowanzozivikanwa se brittle bone chirwere. Muzviitiko zvakakomba, kuputsika kwakawanda kunowanzoitika, nepo imwe nyaya yakapfava inosanganisira kutsemuka kudiki kana mapfupa akatyoka muhupenyu hwemunhu. Vanhu vane chirwere ichi vanozvarwa vasingakwanisi kugadzira tishu dzinobatanidza kana kuva nazvo nekuda kwemajini asina kunaka. Inokanganisa kuumbwa kwe collagen, iyo inobatanidza tishu protein inosimbisa mapfupa. Chirwere ichi chinoitika mumhando I neIX, ini ndiri munyoro uye IX ichiuraya. Chiratidzo chikuru che osteogenesis imperfecta inowanzoputsika. Zvimwe zviratidzo zvinosanganisira majoini akasununguka, kuremara kwemapfupa, kusanzwa, matambudziko ekufema uye matambudziko emazino. Osteogenesis imperfecta inogona kusimbiswa kuburikidza neDNA kana kuongorora collagen.
Iko hakuna marapirwo eizvi nekuti ndeye genetic mamiriro. Kudzidzira muviri uye kurega kusvuta mienzaniso miviri yesarudzo dzemararamiro ane hutano anogona kubatsira kudzivirira kuputsika. Mabhureki, mishonga yekunyaradza marwadzo, uye kutarisirwa kwakafanira kwekutyoka kwemapfupa zvese zvinobatsira. Mishonga inorwisa mabhakitiriya uye antiseptics inogona kushandiswa kurapa hutachiona hwemapfupa. Kuwedzera kudiwa kwemishonga mitsva yekurapa osteogenesis imperfecta uye zvibvumirano zverezinesi uye kudyidzana kwehunyanzvi nevatambi veindasitiri vakakosha mukuvandudza kurapwa kunotarisirwa kukurudzira kukura kwemusika wepasi rose osteogenesis imperfecta kurapwa munguva yekufanotaura.
Kuwedzera mari yekutsvagisa uye yekusimudzira yekugadzira marapirwo matsva uye marapirwo chinhu chakakosha chiri kukurudzira kukura kwemusika wepasi rose osteogenesis imperfecta kurapwa. Zvakare, zvibvumirano zvekupa marezinesi uye kudyidzana kwehunyanzvi nevatambi veindasitiri vakuru mukuvandudza kurapwa kweOI chimwe chinhu chiri kufambisa kukura kwemusika. Uyezve, osteogenesis imperfecta chirwere chemajini, uye nhoroondo yemhuri yevanhu vane OI iri kukonzera kuwedzera kwehuwandu hwezviitiko pasi rose, izvo zvinotarisirwa kufambisa kukura kwemusika.
Semuyenzaniso, muna Chivabvu 2021, Mereo BioPharma Group plc yakazivisa inokurudzira dhata remwedzi mitanhatu kubva muyedzo yekiriniki yeChikamu II-B muvarwere vakuru vane osteogenesis imperfecta type IV, III kana ini ndakarapwa nesetursumab (BPS-6). Sangano reEuropean Medicines Agency (EMA) rakanga ratendera chirongwa chekambani chekuferefeta vana cheBPS-804 uye chine dhizaini yekudzidza yekunyoresa, uye mumiriri wemushonga ave kugadzirira Phase III yehuwandu hwevana.
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